Macrophage Activation Syndrome Secondary to Juvenile Idiopathic Arthritis
نویسندگان
چکیده
منابع مشابه
Macrophage Activation Syndrome as the First Presentation of Juvenile Idiopathic Arthritis
Macrophage activation syndrome (MAS) is a rare feature of rheumatic disorders in children and adolescence and its presentation as the first symptom of rheumatic disorders is very infrequent. A 9-year-old girl, in whom MAS developed, was admitted to our Hospital in Tehran, Iran. She suffered from high grade fever and rash followed by multiple joint swelling months afterwards. Bone marrow aspira...
متن کاملIdiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Alth...
متن کاملMacrophage activation syndrome due to systemic onset juvenile idiopathic arthritis in a case with liver transplantation
Methods A 9-year-old girl (with a liver transplantation because of biliar hypoplasia from her father at the age of five years) presented with fever, rash and oligoarthiritis. An urgent tube thoracostomy was performed because of severe pleural effusion. She was transferred to the intensive care unit with the diagnosis of sepsis. On admission, the patient’s white blood cells (WBC) 31600/mm, plate...
متن کاملPosterior reversible encephalopathy syndrome complicating macrophage activation syndrome in a patient with systemic juvenile idiopathic arthritis
Machrophage activation syndrome (MAS) is a rare and potentially fatal disease, commonly associated with chronic rheumatic diseases, mainly juvenile idiopathic arthritis. It is included in the group of secondary forms of haemophagocytic syndrome, and other causes are lymphoproliferative diseases and infections. Its most important clinical and laboratorial manifestations are non-remitting fever, ...
متن کاملMacrophage activation syndrome in patients with systemic juvenile idiopathic arthritis treated with tocilizumab
Introduction Macrophage activation syndrome (MAS) is a severe, potentially fatal complication of systemic juvenile idiopathic arthritis (sJIA). Changes in therapies, including biologics, have been associated with the onset of MAS. Interleukin-6 (IL-6) plays a major pathogenic role in sJIA; data in animals suggest that high IL-6 levels contribute to the triggering of MAS [1]. Treatment with the ...
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ژورنال
عنوان ژورنال: Turkish Journal of Pediatric Emergency and Intensive Care Medicine
سال: 2016
ISSN: 2146-2399
DOI: 10.4274/cayd.65375